https://doi.org/10.1351/goldbook.13491
Rare systemic inflammatory myopathy, including primary polymyositis, primary dermatomyositis, myositis associated with malignancy, childhood dermatomyositis, and myositis with multisystem autoimmune disease [e.g., mixed connective tissue disease (MCTD), systemic sclerosis (SSc)].
Note: Autoantibodies against aminoacyl-tRNA synthetases (e.g., anti-Jo-1), signal recognition particles (e.g., anti-SRP54), nuclear helicase (anti-Mi-2), tRNA and tRNA–protein complexes (e.g., anti-Mas), and translation factor (anti-KJ) have been described as myositis-specific.