primary biliary cirrhosis

initialism: PBC
https://doi.org/10.1351/goldbook.13600
Autoimmune liver disease that results in the destruction of bile ducts, leading to fibrosis and cirrhosis.
Note: Primary biliary cirrhosis-specific antibodies are antimitochondrial antibodies (AMAs) directed against proteins of the pyruvate dehydrogenase complex (mainly the E2 subunit).
Source:
PAC, 2012, 84, 1113. (IUPAC glossary of terms used in immunotoxicology (IUPAC Recommendations 2012)) on page 1233 [Terms] [Paper]